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Kindler Syndrome with a severe form of periodontal manifestation: A Case Report

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» doi: 10.31838/ecb/2023.12.si6.234


Kindler Syndrome (KS) is an extremely rare genodermatosis characterized by - acral blistering, photosensitivity, progressive poikiloderma, skin atrophy, and diverse forms of mucosal involvement since childhood. An array of dermal and extra dermal features has also been described. We present a 17-year-old patient whose main complaint was about swollen gums that existed for the past 1 year. Intraoral examination revealed pale oral mucosa and a depapillated tongue without significant ankyloglossia. A detailed periodontal charting was performed. The Gingival (GI) and Plaque Index (PI) scores were both 3 and the Oral Hygiene Index - Simplified score was poor. Gingival enlargement (grades 2 and 3) was documented for the upper and lower anterior teeth. The average Probing Pocket Depth (PPD) was approximately 10 mm (deep infra-bony and supra-bony pockets). Clinical Attachment Loss (CAL) was >4 mm. Full mouth extractions were performed as all the teeth were grade 3 mobile. Therefore, young patients with Kindler syndrome and severe periodontal disease must undergo a detailed intraoral examination and receive appropriate periodontal treatment at the earliest.

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